Pulmonary hypertension associated with obliterative phlebitis in IgG4-related lung disease.
نویسندگان
چکیده
IgG4-related disease (IgG4-RD) is a systemic fibroinflammatory disease associated with elevated serum IgG4 level and IgG4-positive plasma cell infiltration into multiple organs [1]. In 2001, HAMANO et al. [2] reported that patients with autoimmune pancreatitis have high-serum IgG4 concentrations. Subsequently, IgG4-related lesions similar to those of autoimmune pancreatitis have been identified in other organs [1] including the lungs [3].
منابع مشابه
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ورودعنوان ژورنال:
- The European respiratory journal
دوره 45 3 شماره
صفحات -
تاریخ انتشار 2015